Williams B
Acta Neurochir (Wien). 1979;47(3-4):187-217. doi: 10.1007/BF01406404.
Three men are presented, all of whom were born with difficulty and later developed severe syringomyelia with collapsing cords on air myelography. Each had hydrocephalus and a sizable subarachnoid pouch in the posterior fossa. The clinical features and investigations are presented with a discussion of the aetiology and possible mechanisms concerned in pathogenesis and treatment. All three men had posterior fossa exploration over fifty years after birth, and the first two were also treated by valved ventriculo-atrial shunts. Each patient has improved a little since operation, but no certainty that this was due to surgery has been proved in any case; none has progressed since the last operation.
本文介绍了三名男性患者,他们出生时均伴有难产情况,随后均发展为严重的脊髓空洞症,空气脊髓造影显示脊髓空洞形成。三人都患有脑积水,后颅窝均有一个较大的蛛网膜囊肿。文中呈现了他们的临床特征和检查结果,并对病因、发病机制及治疗中可能涉及的机制进行了讨论。这三名男性患者均在出生五十多年后接受了后颅窝探查术,前两名患者还接受了带瓣膜的脑室-心房分流术。自手术以来,每位患者都稍有改善,但无论如何都无法确定这是手术所致;自上次手术后,三人病情均未进展。