[综合研究在幼儿脊髓性肌萎缩症诊断中的作用]
[Role of complex studies in the diagnosis of spinal amyotrophy in young children].
作者信息
Zhurba L T, Timonina O V, Aingorn E D, Koroleva I A, Avakian G N
出版信息
Zh Nevropatol Psikhiatr Im S S Korsakova. 1979;79(10):1342-5.
PMID:494907
Abstract
The analysis of a pathomorphological verified case of Werding-Hoffmanns disease and its comparison with the other clinical and EEG data shows that the specific electromyographical traits of the spinal lesion in some patients are revealed in a late period. For the differentiation of the essential muscular and the secondary neurogenic lesions in the early stages of the disease the morphological studies of muscular bioptic specimens are very important.
摘要
对一例经病理形态学证实的韦丁-霍夫曼病病例的分析及其与其他临床和脑电图数据的比较表明，部分患者脊髓病变的特定肌电图特征在疾病晚期才显现出来。对于在疾病早期区分原发性肌肉病变和继发性神经源性病变，肌肉活检标本的形态学研究非常重要。
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