[Role of complex studies in the diagnosis of spinal amyotrophy in young children].

The analysis of a pathomorphological verified case of Werding-Hoffmanns disease and its comparison with the other clinical and EEG data shows that the specific electromyographical traits of the spinal lesion in some patients are revealed in a late period. For the differentiation of the essential muscular and the secondary neurogenic lesions in the early stages of the disease the morphological studies of muscular bioptic specimens are very important.