Excretion of alpha-keto-delta-guanidinovaleric acid and its cyclic form in patients with hyperargininemia.
作者信息
Marescau B, Pintens J, Lowenthal A, Terheggen H G
出版信息
Clin Chim Acta. 1979 Oct 15;98(1-2):35-8. doi: 10.1016/0009-8981(79)90162-1.
PMID:498528
Abstract
alpha-Keto-delta-guanidinovaleric acid, in equilibrium with its cyclic form, has been identified in the urines of three sisters affected with hyperargininemia. Identification was achieved on the basis of its similarity with the enzymatically synthesized compounds.
摘要
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