Gilbert S, Spellacy E, Watts R W
Dev Med Child Neurol. 1979 Dec;21(6):795-800. doi: 10.1111/j.1469-8749.1979.tb01704.x.
The results are described of a behavioural programme designed to modify self-injurious behaviour of a child with Lesch-Nyhan syndrome. The treatment combined extinction of the injurious behaviour and reinforcement of alternative behaviour, and was successful in the controlled hospital environment. However, an attempt to teach the parents to continue the treatment at home failed. The results are discussed in terms of the possible relationship between organic and environmental factors in maintaining the injurious behaviour, and the importance of analysing both the behaviour itself and the factors (including familial) maintaining it. It is suggested that parents should be advised about management of behavioural problems at an early age.
本文描述了一项旨在改变患有莱施-奈恩综合征儿童自伤行为的行为计划的结果。该治疗方法结合了对伤害行为的消退和对替代行为的强化，在可控的医院环境中取得了成功。然而，教导家长在家中继续进行治疗的尝试失败了。本文从维持伤害行为的器质性因素和环境因素之间可能存在的关系，以及分析行为本身和维持该行为的因素（包括家庭因素）的重要性方面对结果进行了讨论。建议应在儿童早期就向家长提供有关行为问题管理的建议。
