The metabolism of sphingomyelin. II. Evidence of an enzymatic deficiency in Niemann-Pick diseae.
作者信息
Brady R O, Kanfer J N, Mock M B, Fredrickson D S
出版信息
Proc Natl Acad Sci U S A. 1966 Feb;55(2):366-9. doi: 10.1073/pnas.55.2.366.
Abstract
摘要
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Proc Natl Acad Sci U S A. 1966 Feb;55(2):366-9. doi: 10.1073/pnas.55.2.366.
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Phosphorylcholine in rat tissues.大鼠组织中的磷酰胆碱。
Biochem J. 1955 Jun;60(2):325-8. doi: 10.1042/bj0600325.
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METABOLISM OF GLUCOCEREBROSIDES. II. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN GAUCHER'S DISEASE.葡萄糖脑苷脂的代谢。II. 戈谢病中酶缺乏的证据。
Biochem Biophys Res Commun. 1965 Jan 18;18:221-5. doi: 10.1016/0006-291x(65)90743-6.
3
Rapid sensitive method for determining H3-water in body fluids by liquid scintillation spectrometry.通过液体闪烁光谱法测定体液中H3-水的快速灵敏方法。
Proc Soc Exp Biol Med. 1959 Oct;102:8-12. doi: 10.3181/00379727-102-25125.
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Sphingomyelin synthesis in Niemann-Pick disease.尼曼-匹克病中的鞘磷脂合成
Am J Clin Nutr. 1961 Jan-Feb;9:63-7. doi: 10.1093/ajcn/9.1.63.
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