培养的正常成纤维细胞以及来自A型和C型尼曼-匹克病患者的成纤维细胞对鞘磷脂的原位降解 - Suppr

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超能文献

In situ degradation of sphingomyelin by cultured normal fibroblasts and fibroblasts from patients with Niemann-Pick disease type A and C.

作者信息

Maziere J C, Maziere C, Mora L, Routier J D, Polonovski J

出版信息

Biochem Biophys Res Commun. 1982 Oct 15;108(3):1101-6. doi: 10.1016/0006-291x(82)92113-1.

DOI:10.1016/0006-291x(82)92113-1

PMID:7181884

Abstract

摘要

相似文献

In situ degradation of sphingomyelin by cultured normal fibroblasts and fibroblasts from patients with Niemann-Pick disease type A and C.培养的正常成纤维细胞以及来自A型和C型尼曼-匹克病患者的成纤维细胞对鞘磷脂的原位降解

Biochem Biophys Res Commun. 1982 Oct 15;108(3):1101-6. doi: 10.1016/0006-291x(82)92113-1.

Metabolism of sphingomyelin in cultured skin fibroblasts from patients with different types of Niemann-Pick disease.不同类型尼曼-匹克病患者培养皮肤成纤维细胞中鞘磷脂的代谢

Tohoku J Exp Med. 1986 Apr;148(4):365-71. doi: 10.1620/tjem.148.365.

Uptake and metabolism of radioactively labeled sphingomyelin in cultured skin fibroblasts from controls and patients with Niemann-Pick disease and other lysosomal storage diseases.来自对照个体以及患有尼曼-匹克病和其他溶酶体贮积病患者的培养皮肤成纤维细胞中放射性标记鞘磷脂的摄取与代谢

Biochim Biophys Acta. 1983 Nov 1;754(1):82-92. doi: 10.1016/0005-2760(83)90084-x.

Stimulation of sphingomyelin hydrolysis by cannabidiol in fibroblasts from a Niemann-Pick patient.大麻二酚对尼曼-匹克病患者成纤维细胞中鞘磷脂水解的刺激作用。

Biochem Biophys Res Commun. 1984 May 31;121(1):168-73. doi: 10.1016/0006-291x(84)90702-2.

Uptake and intracellular degradation of fluorescent sphingomyelin by fibroblasts from normal individuals and a patient with Niemann-Pick disease.正常个体和一名尼曼-匹克病患者的成纤维细胞对荧光鞘磷脂的摄取及细胞内降解

Biochim Biophys Acta. 1987 Apr 24;918(3):250-9. doi: 10.1016/0005-2760(87)90228-1.

Metabolism of sphingomyelin by intact cultured fibroblasts: differentiation of Niemann-Pick disease type A and B.完整培养的成纤维细胞对鞘磷脂的代谢：A型和B型尼曼-匹克病的鉴别

Biochem Biophys Res Commun. 1982 Mar 15;105(1):14-9. doi: 10.1016/s0006-291x(82)80004-1.

Lysosomal involvement in cellular turnover of plasma membrane sphingomyelin.溶酶体参与质膜鞘磷脂的细胞更新。

Biochim Biophys Acta. 1984 Apr 18;793(2):169-79. doi: 10.1016/0005-2760(84)90318-7.

Pathways of sphingomyelin metabolism in cultured fibroblasts from normal and sphingomyelin lipidosis subjects.正常人和鞘磷脂沉积症患者培养成纤维细胞中鞘磷脂代谢途径

J Biol Chem. 1983 Jul 25;258(14):8595-600.

Uptake and degradation of several pyrenesphingomyelins by skin fibroblasts from control subjects and patients with Niemann-Pick disease. Effect of the structure of the fluorescent fatty acyl residue.来自对照受试者和尼曼-匹克病患者的皮肤成纤维细胞对几种芘神经鞘磷脂的摄取和降解。荧光脂肪酰基残基结构的影响。

Biochem J. 1991 Apr 1;275 ( Pt 1)(Pt 1):211-7. doi: 10.1042/bj2750211.

Biochemical studies in Niemann-Pick disease. III. In vitro and in vivo assays of sphingomyelin degradation in cultured skin fibroblasts and amniotic fluid cells for the diagnosis of the various forms of the disease.尼曼-匹克病的生化研究。III. 用于诊断该疾病各种类型的培养皮肤成纤维细胞和羊水细胞中鞘磷脂降解的体外和体内测定

Clin Genet. 1985 Jan;27(1):20-32. doi: 10.1111/j.1399-0004.1985.tb00180.x.

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Molecular Targets of Cannabidiol in Neurological Disorders.大麻二酚在神经疾病中的分子靶点

Neurotherapeutics. 2015 Oct;12(4):699-730. doi: 10.1007/s13311-015-0377-3.

Improvement in lipid and protein trafficking in Niemann-Pick C1 cells by correction of a secondary enzyme defect.通过纠正次要酶缺陷改善尼曼-匹克 C1 细胞中的脂质和蛋白质转运。

Traffic. 2010 May;11(5):601-15. doi: 10.1111/j.1600-0854.2010.01046.x. Epub 2010 Feb 22.

Niemann-Pick disease type C. Study on the nature of the cerebral storage process.尼曼-匹克病C型。大脑储存过程本质的研究。

Acta Neuropathol. 1985;66(4):325-36. doi: 10.1007/BF00690966.

Alterations in cholesterol metabolism in cultured fibroblasts from patients with Niemann-Pick disease type C.C型尼曼-匹克病患者培养成纤维细胞中胆固醇代谢的改变。

J Inherit Metab Dis. 1987;10(4):339-46. doi: 10.1007/BF01799976.

A new variant of sphingomyelinase deficiency (Niemann-Pick): visceromegaly, minimal neurological lesions and low in vivo degradation rate of sphingomyelin.鞘磷脂酶缺乏症（尼曼-匹克病）的一种新变体：内脏肿大、轻微神经病变以及鞘磷脂体内降解率低。

J Inherit Metab Dis. 1986;9(4):357-66. doi: 10.1007/BF01800485.

Enzyme activities and phospholipid storage patterns in brain and spleen samples from Niemann-Pick disease variants: a comparison of neuropathic and non-neuropathic forms.尼曼-匹克病变体脑和脾样本中的酶活性及磷脂储存模式：神经病变型与非神经病变型的比较

J Inherit Metab Dis. 1986;9(1):59-71. doi: 10.1007/BF01813904.

Sorting of an internalized plasma membrane lipid between recycling and degradative pathways in normal and Niemann-Pick, type A fibroblasts.正常及A型尼曼-匹克病成纤维细胞中内化质膜脂质在再循环和降解途径之间的分选

J Cell Biol. 1990 Aug;111(2):429-42. doi: 10.1083/jcb.111.2.429.

The role of sphingomyelin in phosphatidylcholine metabolism in cultured human fibroblasts from control and sphingomyelin lipidosis patients and in Chinese hamster ovary cells.鞘磷脂在来自对照人群和鞘磷脂脂质沉积症患者的培养人成纤维细胞以及中国仓鼠卵巢细胞的磷脂酰胆碱代谢中的作用。

Biochem J. 1990 Jun 15;268(3):719-24. doi: 10.1042/bj2680719.

Bone marrow transplantation for Niemann-Pick type IA disease.用于治疗A型尼曼-匹克病的骨髓移植

J Inherit Metab Dis. 1992;15(6):919-28. doi: 10.1007/BF01800234.

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