Beighton P H, Murdoch J L, Votteler T
Gut. 1969 Dec;10(12):1004-8. doi: 10.1136/gut.10.12.1004.
The gastrointestinal abnormalities encountered in 125 patients with the Ehlers-Danlos syndrome have been described. Spontaneous perforation of the intestine and massive gastrointestinal haemorrhage are uncommon but potentially lethal complications of the Ehlers-Danlos syndrome. Less dangerous abnormalities, such ;as external hernia, hiatus hernia, eventration of the diaphragm, intestinal diverticula, and rectal prolapse were all encountered in patients in the series. Abdominal surgery in affected patients may be made difficult by fragility of tissues and a bleeding tendency. In the postoperative period, tearing out of sutures and wound dehiscence may occur.
本文描述了125例埃勒斯-当洛综合征患者所出现的胃肠道异常情况。肠道自发性穿孔和大量胃肠道出血并不常见，但却是埃勒斯-当洛综合征潜在的致命并发症。该系列患者中还出现了一些危险性较小的异常情况，如腹股沟疝、食管裂孔疝、膈膨出、肠憩室和直肠脱垂。由于组织脆弱和出血倾向，对患病患者进行腹部手术可能会变得困难。在术后阶段，可能会发生缝线撕裂和伤口裂开。
