网状细胞发育不全：两兄弟的病例报告。
Reticular dysgenesis: report of two brothers.
作者信息
Español T, Compte J, Alvarez C, Tallada N, Laverde R, Peguero G
出版信息
Clin Exp Immunol. 1979 Dec;38(3):615-20.
Abstract
We describe two brothers with marked leucopenia, lymphopenia, no immunologicl response to infections (no Ig production, negative PHA response and very low number of T and B lymphocytes in peripheral blood) and hypocellular marrow. They died at 12 and 8 days of life with infection (E. coli and Klebsiella, respectively).
摘要
我们描述了两名患有明显白细胞减少症、淋巴细胞减少症、对感染无免疫反应（无免疫球蛋白产生、PHA反应阴性且外周血中T和B淋巴细胞数量极低）以及骨髓细胞减少的兄弟。他们分别在出生后12天和8天因感染（分别为大肠杆菌和克雷伯菌）死亡。
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