Einola S, Aho A J, Lauren P, Satokari K
Acta Chir Scand. 1979;145(8):563-9.
Three cases of desmoid tumour in a lower extremity are described. Primary radical excision is necessary for this type of tumour, because of its clear tendency to recur. In the described cases surgery was complicated by the proximity of neural structures and blood vessels. Preoperative angiography was useful for determining the size of the tumour and its position in relation to large blood vessels. Pathologic vascularity was found in the tumours, but histologic examination revealed no sign of malignancy. The histologic structure of the tumours corresponded in all respects to benign fibromatosis, apart from a clear increase in the number of mast cells. The tumours showed a tendency to grow between the muscle fibres, though a pseudocapsule was observed at operation in two cases. None of the specimens from the extirpation line displayed any signs of tumour tissue, but this did not preclude recurrence.
本文描述了三例下肢硬纤维瘤病例。由于这类肿瘤明显的复发倾向,原发性根治性切除是必要的。在所描述的病例中,手术因神经结构和血管位置临近而变得复杂。术前血管造影有助于确定肿瘤大小及其与大血管的位置关系。肿瘤中发现了病理性血管,但组织学检查未显示恶性迹象。除肥大细胞数量明显增加外,肿瘤的组织结构在各方面均与良性纤维瘤病相符。肿瘤有在肌纤维间生长的倾向,不过在两例手术中观察到有假包膜。切除线处的标本均未显示任何肿瘤组织迹象,但这并不排除复发的可能。