Rosenberg E, Lang R, Boisseau V, Rojanasathit S, Avioli L V
J Clin Endocrinol Metab. 1977 Feb;44(2):346-55. doi: 10.1210/jcem-44-2-346.
10 children with osteogenesis imperfecta, 4 with "tarda" and 6 with "congenita" varieties of the disease, were treated with salmon calcitonin (SCT) for intervals ranging from 14 to 35 months. Responses to SCT therapy in patients with osteogenesis imperfecta tarda were characterized by an apparent decreased fracture incidence in three, a fall in either alkaline or acid phosphatase, and a rate of increase in forearm bone mass which was greater than that observed in an untreated "tarda" population. The chemical response SCT therapy varied in children with osteogenesis imperfecta congenita, only one demonstrating a decrease in both acid phosphatase and urinary hydroxyproline. Three others responded with a rise in acid phosphatase, two of whom also demonstrated a fall in urinary hydroxyproline; in two other "congenita" patients urinary hydroxyproline was actually higher after SCT treatment and acid phosphatase relatively unchanged. Alkaline phosphatase was normal in all "congenita" patients before and following the SCT treatment interval. These varied biochemical responses were associated with temporary increments in bone mass early in the treatment course, although in bone mass early in the treatment course, although one "congenita" patient with the largest calciuric response to SCT and an increase in hydroxyproline excretion demonstrated progressive increments in skeletal mineral content during a 14-month treatment interval. In both "tarda" and "congenita" subjects, parathyroid hormone was unchanged by chronic SCT treatment; SCT-antibodies were detectable although biological responsivity to SCT persisted.
10名成骨不全患儿接受了鲑鱼降钙素(SCT)治疗,治疗时间为14至35个月,其中4名患有“迟发型”,6名患有“先天型”。迟发型成骨不全患者对SCT治疗的反应表现为:3例骨折发生率明显降低,碱性磷酸酶或酸性磷酸酶下降,前臂骨量增加速率高于未治疗的“迟发型”患者群体。先天型成骨不全患儿对SCT治疗的化学反应各不相同,只有1例酸性磷酸酶和尿羟脯氨酸均下降。另外3例酸性磷酸酶升高,其中2例尿羟脯氨酸也下降;另外2例“先天型”患者在SCT治疗后尿羟脯氨酸实际上更高,酸性磷酸酶相对未变。在SCT治疗前后,所有“先天型”患者的碱性磷酸酶均正常。这些不同的生化反应与治疗早期骨量的暂时增加有关,尽管在治疗早期骨量有所增加,尽管1例对SCT有最大钙尿反应且羟脯氨酸排泄增加的“先天型”患者在14个月的治疗期间骨骼矿物质含量逐渐增加。在“迟发型”和“先天型”患者中,慢性SCT治疗后甲状旁腺激素均未改变;尽管对SCT的生物学反应持续存在,但仍可检测到SCT抗体。