缺乏次黄嘌呤 - 鸟嘌呤磷酸核糖转移酶的人成纤维细胞中嘌呤从头合成加速的生化基础。 - Suppr

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超能文献

Biochemical bases of accelerated purine biosynthesis de novo in human fibroblasts lacking hypoxanthine-guanine phosphoribosyltransferase.

作者信息

Rosenbloom F M, Henderson J F, Caldwell I C, Kelley W N, Seegmiller J E

出版信息

J Biol Chem. 1968 Mar 25;243(6):1166-73.

PMID:5650894

Abstract

摘要

相似文献

Biochemical bases of accelerated purine biosynthesis de novo in human fibroblasts lacking hypoxanthine-guanine phosphoribosyltransferase.缺乏次黄嘌呤 - 鸟嘌呤磷酸核糖转移酶的人成纤维细胞中嘌呤从头合成加速的生化基础。

J Biol Chem. 1968 Mar 25;243(6):1166-73.

Accelerated purine biosynthesis de novo in skin fibroblasts deficient in hypoxanthine--guanine phosphoribosyltransferase activity.

Biochim Biophys Acta. 1968 Aug 23;166(1):258-60. doi: 10.1016/0005-2787(68)90512-1.

Mechanism of excessive purine biosynthesis in hypoxanthine-guanine phosphoribosyltransferase deficiency.次黄嘌呤-鸟嘌呤磷酸核糖转移酶缺乏症中嘌呤生物合成过多的机制。

J Clin Invest. 1970 May;49(5):968-78. doi: 10.1172/JCI106316.

A new assay method for hypoxanthine-guanine phosphoribosyltransferase.一种次黄嘌呤-鸟嘌呤磷酸核糖转移酶的新检测方法。

J Lab Clin Med. 1970 Nov;76(5):733-8.

Role of glutamine in purine synthesis and in guanine nucleotide formation in normal fibroblasts and in fibroblasts deficient in hypoxanthine phosphoribosyltransferase activity.

Biochim Biophys Acta. 1973 Mar 19;299(2):283-92. doi: 10.1016/0005-2787(73)90351-1.

Hyperuricaemia and choreoathetosis in a child without mental retardation or self-mutilation - a new HPRT variant.一名无智力障碍或自残行为儿童的高尿酸血症和舞蹈手足徐动症——一种新的次黄嘌呤-鸟嘌呤磷酸核糖转移酶（HPRT）变异型

J Inherit Metab Dis. 1982;5(4):183-6. doi: 10.1007/BF02179135.

Effects of the uricogenic agent, 2-ethylamino-1,3,4-thiadiazole in hypoxanthine-guanine phosphoribosyl transferase deficiency.尿酸生成剂2-乙氨基-1,3,4-噻二唑在次黄嘌呤-鸟嘌呤磷酸核糖转移酶缺乏症中的作用。

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Salvage and interconversion of purines in developing Artemia.

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Enzyme defect associated with a sex-linked human neurological disorder and excessive purine synthesis.与一种X连锁人类神经疾病及嘌呤过度合成相关的酶缺陷。

Science. 1967 Mar 31;155(3770):1682-4. doi: 10.1126/science.155.3770.1682.

INHIBITION OF PRUINE PHOSPHORIBOSYLTRANSFERASES OF EHRLICH ASCITES-TUMOUR CELLS BY 6-MERCAPTOPURINE.6-巯基嘌呤对艾氏腹水癌细胞嘌呤磷酸核糖转移酶的抑制作用

Biochem J. 1965 Jan;94(1):64-70. doi: 10.1042/bj0940064.

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