Klinenberg J R
Calif Med. 1969 Mar;110(3):231-44.
Recent studies have confirmed that gout is an inborn error of metabolism. It has now become evident that the hyperuricemia associated with gout might occur either due to overproduction of uric acid, underexcretion of uric acid or a combination of these processes. Furthermore, patients with excessive purine synthesis may have a specific enzyme defect resulting in altered feedback inhibition of purine synthesis. A neurological disease manifest by mental retardation, choreo-athetosis, aggressive behavior, lip-biting and self-mutilation and associated with decidedly increased purine biosynthesis serves as a prototype of this kind of disorder. Other defects in regulation of purine biosynthesis have been postulated but their existence not yet confirmed. It has been demonstrated that urate crystals which are deposited from hyperuricemic body fluids set up an acute inflammatory reaction by means of a variety of chemical mediators. Thus, acute gouty arthritis is now recognized as an example of "crystal induced" synovitis. The treatment of gout consists of (1) the control of acute gouty attacks, and (2) the maintenance of normal serum uric acid concentrations. This latter may be achieved either with uricosuric drugs or with xanthine oxidase inhibition. With these principles in mind, it is now possible to avoid many of the severe crippling effects of gout and to restore the vast majority of gouty patients to useful and productive lives.
近期研究已证实痛风是一种先天性代谢紊乱。现在已经很明显,与痛风相关的高尿酸血症可能是由于尿酸生成过多、尿酸排泄过少或这些过程的综合作用所致。此外,嘌呤合成过多的患者可能存在特定的酶缺陷,导致嘌呤合成的反馈抑制改变。一种以智力发育迟缓、舞蹈手足徐动症、攻击行为、咬唇和自残为特征且与嘌呤生物合成明显增加相关的神经疾病,就是这类疾病的一个典型例子。有人推测嘌呤生物合成调节存在其他缺陷,但尚未得到证实。已经证明,从高尿酸血症体液中沉积的尿酸盐晶体通过多种化学介质引发急性炎症反应。因此,急性痛风性关节炎现在被认为是“晶体诱导”滑膜炎的一个例子。痛风的治疗包括:(1)控制急性痛风发作;(2)维持正常的血清尿酸浓度。后者可以通过促尿酸排泄药物或黄嘌呤氧化酶抑制来实现。牢记这些原则,现在就有可能避免痛风的许多严重致残影响,并使绝大多数痛风患者恢复到有益和有生产能力的生活。