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急性韦格纳肉芽肿病。

Acute Wegener's granulomatosis.

作者信息

Leak D, Clein G P

出版信息

Thorax. 1967 Sep;22(5):437-43. doi: 10.1136/thx.22.5.437.

DOI:10.1136/thx.22.5.437
PMID:6050291
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC471682/
Abstract

Two cases of acute Wegener's granulomatosis are described. The first ended fatally after an illness of only two weeks. In the second a remission of three years has been obtained with heavy doses of steroid. At present there is evidence of impaired pulmonary gas transfer and also chronic glomerulonephritis, but the patient is asymptomatic. When the disease presents with pulmonary cavitation it may be confused with pulmonary neoplasm, tuberculosis, or lung abscess, and the diagnosis is made by biopsy. The Rose-Waaler was strongly positive in the case tested.

摘要

本文描述了两例急性韦格纳肉芽肿病。第一例在患病仅两周后死亡。第二例通过大剂量类固醇治疗已缓解三年。目前有肺气体交换受损及慢性肾小球肾炎的证据,但患者无症状。当该病表现为肺空洞时,可能会与肺肿瘤、肺结核或肺脓肿相混淆,诊断需通过活检确定。检测的病例中罗斯 - 瓦勒试验呈强阳性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/35330ffb2b87/thorax00095-0054-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/9fb1b795a6a5/thorax00095-0052-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/eee0f7ec0009/thorax00095-0052-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/992df0843128/thorax00095-0053-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/ed5a437abce2/thorax00095-0053-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/2d398f849f64/thorax00095-0054-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/35330ffb2b87/thorax00095-0054-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/9fb1b795a6a5/thorax00095-0052-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/eee0f7ec0009/thorax00095-0052-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/992df0843128/thorax00095-0053-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/ed5a437abce2/thorax00095-0053-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/2d398f849f64/thorax00095-0054-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7de9/471682/35330ffb2b87/thorax00095-0054-b.jpg

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1
Acute Wegener's granulomatosis.急性韦格纳肉芽肿病。
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2
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8
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9
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本文引用的文献

1
Chronic Granuloma Associated with Periarteritis Nodosa: Report of a Case with Renal Failure.与结节性多动脉炎相关的慢性肉芽肿:一例肾衰竭病例报告
Am J Pathol. 1944 Nov;20(6):1057-71.
2
AUTO-ANTIBODY STUDIES IN INTERSTITIAL PULMONARY FIBROSIS.间质性肺纤维化中的自身抗体研究。
Br Med J. 1965 Apr 3;1(5439):886-91. doi: 10.1136/bmj.1.5439.886.
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A PATIENT WITH WEGENER'S GRANULOMATOSIS EXHIBITING UNUSUAL CLINICAL AND MORPHOLOGIC FEATURES.
Am J Med. 1964 Aug;37:311-9. doi: 10.1016/0002-9343(64)90014-2.
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CLASSIFICATION AND ETIOLOGIC ASPECTS OF NECROTIZING ANGIITIDES: AN ANALYTIC APPROACH TO A CONFUSED SUBJECT WITH A CRITICAL REVIEW OF THE EVIDENCE FOR HYPERSENSITIVITY IN POLYARTERITIS NODOSA.坏死性血管炎的分类与病因学方面:对一个复杂主题的分析方法及对结节性多动脉炎中过敏反应证据的批判性综述
Mayo Clin Proc. 1964 Mar;39:205-22.
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WEGENER'S GRANULOMATOSIS. A CLINICO-PATHOLOGIC STUDY OF FOUR CASES.
Ann Intern Med. 1963 Oct;59:521-30. doi: 10.7326/0003-4819-59-4-521.
6
WEGENER'S GRANULOMATOSIS; PROLONGED THERAPY WITH LARGE DOSES OF STEROIDS.韦格纳肉芽肿;大剂量类固醇的长期治疗。
JAMA. 1963 Nov 30;186:827-30.
7
Wegener's granulomatosis. Report of two cases and brief review.
Arch Intern Med. 1961 Aug;108:269-78. doi: 10.1001/archinte.1961.03620080101010.
8
Giant-cell granuloma of the respiratory tract (Wegener's granulomatosis).呼吸道巨细胞肉芽肿(韦格纳肉芽肿)
Br Med J. 1958 Aug 2;2(5091):265-70. doi: 10.1136/bmj.2.5091.265.
9
Polyarteritis nodosa.结节性多动脉炎
Q J Med. 1957 Jan;26(101):43-81.
10
Wegener's granulomatosis: pathology and review of the literature.韦格纳肉芽肿病:病理学及文献综述
AMA Arch Pathol. 1954 Dec;58(6):533-53.