Guberti A, Marchi M, Tartari S, Pavani A, Franchella A, Georgacopulo P
Minerva Med. 1984 Nov 10;75(43):2617-21.
Sickle cell anaemia is the most common hereditary haemoglobin pathology. It is found in either a homozygous or heterozygous form, associated in the latter case with other haemoglobinopathies. In view of the pathogenesis and the various related imbalances, amply confirmed by others, which can well prove disastrous, the pre, per and post-operative precautions to be adopted in such patients are assessed.
镰状细胞贫血是最常见的遗传性血红蛋白病。它以纯合子或杂合子形式出现,在后一种情况下与其他血红蛋白病相关。鉴于其发病机制以及各种相关的失衡情况,已被其他人充分证实,这些情况可能会造成灾难性后果,因此对这类患者术前、术中及术后应采取的预防措施进行了评估。