Scharnetzky M, Schröter W
Monatsschr Kinderheilkd. 1980 Dec;128(12):780-2.
Hereditary pancreatitis was diagnosed in dystrophic boy at the age of 2 1/2 years after recurring episodes of severe abdominal pain. Extensive left-sided pleural effusions caused surgical exploration. Pancreatography showed typical dilation of the pancreatic ductal system. After hemipancreatectomy by the boy recovered very fast. Characteristic features in diagnosing of hereditary pancreatitis are the onset of recurring attacks of abdominal pain in early childhood and anatomical defects in the pancreatic ductal system. The disease shows variability between family members.
一名营养不良的男孩在2岁半时因反复出现严重腹痛被诊断为遗传性胰腺炎。大量左侧胸腔积液促使进行手术探查。胰管造影显示胰管系统典型扩张。男孩接受半胰切除术后恢复得非常快。遗传性胰腺炎诊断的特征性表现是儿童早期反复出现腹痛发作以及胰管系统的解剖学缺陷。该病在家庭成员之间表现出变异性。
