Cytochrome-C-oxidase deficiency in muscles of a floppy infant without mitochondrial myopathy.

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作者信息

Rimoldi M, Bottacchi E, Rossi L, Cornelio F, Uziel G, Di Donato S

出版信息

J Neurol. 1982;227(4):201-7. doi: 10.1007/BF00313387.

DOI:10.1007/BF00313387

PMID:6183406

Abstract

摘要

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Protein measurement with the Folin phenol reagent.使用福林酚试剂进行蛋白质测定。

J Biol Chem. 1951 Nov;193(1):265-75.

An electron-transport system associated with the outer membrane of liver mitochondria. A biochemical and morphological study.与肝线粒体外膜相关的电子传递系统。一项生化与形态学研究。

J Cell Biol. 1967 Feb;32(2):415-38. doi: 10.1083/jcb.32.2.415.

Friedreich's ataxia in northern Italy. II. Biochemical studies in cultured cells.意大利北部的弗里德赖希共济失调。II. 培养细胞中的生化研究。

Can J Neurol Sci. 1980 Nov;7(4):409-12. doi: 10.1017/s0317167100022964.

Fatal infantile mitochondrial myopathy and renal dysfunction due to cytochrome-c-oxidase deficiency.由于细胞色素c氧化酶缺乏导致的致命性婴儿线粒体肌病和肾功能障碍。

Neurology. 1980 Aug;30(8):795-804. doi: 10.1212/wnl.30.8.795.

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Nondroplet ultrastructural demonstration of cytochrome oxidase activity with a polymerizing osmiophilic reagent, diaminobenzidine (DAB).用聚合嗜锇试剂二氨基联苯胺（DAB）对细胞色素氧化酶活性进行非滴状超微结构演示。

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Arch Neurol. 1973 Sep;29(3):162-9. doi: 10.1001/archneur.1973.00490270044007.

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