Kekomäki M, Ekfors T O, Nikkanen V, Vilkki P
J Pediatr Surg. 1984 Jun;19(3):312-4. doi: 10.1016/s0022-3468(84)80196-7.
We report a primary endodermal sinus tumor (EST) of the right hemidiaphragm, presenting as a right-sided hemothorax in an 18-month-old female. Four operations were performed, the last three being indicated solely by an elevated level of serum alpha-fetoprotein (AFP). Cyclic chemotherapy with varying drug combinations together with irradiation therapy were not effective in controlling the disease. To our knowledge, this is the first instance of a primary EST arising from the diaphragm.
我们报告一例发生于右半膈的原发性内胚窦瘤（EST），该病例为一名18个月大的女性，表现为右侧血胸。患者接受了四次手术，后三次手术完全是由于血清甲胎蛋白（AFP）水平升高而进行的。采用不同药物组合的周期性化疗以及放射治疗均未能有效控制病情。据我们所知，这是首例起源于膈肌的原发性内胚窦瘤。
