Pierce R N, Smith G J
Chest. 1978 Jan;73(1):79-84. doi: 10.1378/chest.73.1.79.
Degos' disease (malignant atrophic papulosis) is a rare multisystemic disease with characteristic cutaneous lesions, abdominal symptoms and often rapidly fatal course. Our review of the reported intrathoracic involvement in the more than 60 reported cases of Degos' disease suggests that pleuritis and pericarditis are manifestations of the underlying pathophysiologic process. Seventeen of these reported cases were said to have intrathoracic lesions, which were, in most cases, incidental findings at autopsy. We present an illustrative report of a case in which chronic pleuritis and pericarditis were the major causes of morbidity in a 32-year-old woman with Degos' disease.
迪戈斯病（恶性萎缩性丘疹病）是一种罕见的多系统疾病，具有特征性皮肤损害、腹部症状，且病程往往进展迅速、可致命。我们对60多例已报道的迪戈斯病病例中胸腔受累情况的回顾表明，胸膜炎和心包炎是潜在病理生理过程的表现。这些已报道病例中有17例据说存在胸腔病变，大多数情况下，这些病变是尸检时的偶然发现。我们报告一例具有代表性的病例，一名32岁患迪戈斯病的女性，其慢性胸膜炎和心包炎是发病的主要原因。
