Casparie M K, Meyer J W, van Huystee B E, Kneppelhout J, Mulder C J
Department of Gastroenterology, Rijnstate Hospital, Arnhem, The Netherlands.
Endoscopy. 1991 Jul;23(4):231-3. doi: 10.1055/s-2007-1010665.
The case is reported of a 69-year-old female with atrophic papules on the skin who developed multiple spontaneous intestinal perforations of which she eventually died. The skin lesions in combination with lesions in the gastrointestinal tract are typical for Degos' disease or malignant atrophic papulosis. The characteristic histopathological and endoscopic features of this rare disease are reported. This case demonstrates the importance of routinely performing endoscopy in Degos' disease to detect silent perforation, even in patients without gastrointestinal complaints.
报告了一例69岁女性患者，其皮肤出现萎缩性丘疹，并发生多处自发性肠穿孔，最终死亡。皮肤病变与胃肠道病变相结合是德戈斯病或恶性萎缩性丘疹病的典型表现。报告了这种罕见疾病的特征性组织病理学和内镜特征。该病例表明，即使在没有胃肠道症状的患者中，对德戈斯病患者常规进行内镜检查以检测隐匿性穿孔也很重要。
