Burton B K, Dillard R G
Am J Med Genet. 1984 Mar;17(3):669-72. doi: 10.1002/ajmg.1320170319.
We report on an infant with the prune belly syndrome who was unusual in that the typical manifestations of the disorder were accompanied by an anterior abdominal wall defect. We speculate that this defect may have occurred as a result of splitting of the abdominal wall secondary to massive bladder dilatation and stretching of the abdominal muscles. An alternative explanation is that the defect may have been the result of secondary pressure necrosis from stretching forces or from contact with another structure, such as the cervix. This case lends further support to the hypothesis that bladder distention with overdistention of the abdomen may be the primary event leading to the findings observed in the prune belly syndrome.
我们报告了一名患有梅干腹综合征的婴儿，该病例的不同寻常之处在于，该疾病的典型表现伴有前腹壁缺损。我们推测，这种缺损可能是由于巨大膀胱扩张和腹肌拉伸导致腹壁裂开所致。另一种解释是，该缺损可能是拉伸力或与其他结构（如子宫颈）接触引起的继发性压力性坏死的结果。该病例进一步支持了以下假说：膀胱扩张伴腹部过度扩张可能是导致梅干腹综合征所见表现的主要原因。
