Neri A, Brugiatelli M, Iacopino P, Callea V, Ronco F
Acta Haematol. 1984;71(4):263-9. doi: 10.1159/000206598.
Natural killer (NK) cell activity against K562 cell targets and the distribution of T cell subpopulations were investigated in the peripheral blood of 25 patients affected by beta thalassemia major, 18 clinically healthy heterozygotes, and 25 age-matched normal subjects. It was found that thalassemia major patients display augmented levels of NK activity [specific lysis 41.9 +/- (se) 4.5%], while thalassemic carriers behave as normal controls [specific lysis 34.6 +/- (se) 3.5%]. The increase of NK function was neither related to the splenectomy nor to the siderosis, but rather to the age and the amount of blood units that the patients had received. An imbalance of circulating T subsets with the helper/suppressor cell ratio significantly diminished (p less than 0.001) was also detected in homozygotes but not in carriers. The finding that NK function is enhanced in homozygous beta thalassemia might be of clinical interest in assessing the risk of development of malignancies in these patients.
研究了25例重型β地中海贫血患者、18例临床健康的杂合子以及25例年龄匹配的正常受试者外周血中自然杀伤(NK)细胞对K562细胞靶标的活性以及T细胞亚群的分布。结果发现,重型地中海贫血患者的NK活性水平升高[特异性裂解率为41.9±(标准误)4.5%],而地中海贫血携带者的表现与正常对照组相似[特异性裂解率为34.6±(标准误)3.5%]。NK功能的增加既与脾切除术无关,也与铁沉着症无关,而是与患者的年龄和接受的血液单位量有关。在纯合子中还检测到循环T亚群失衡,辅助/抑制细胞比例显著降低(p<0.001),而在携带者中未检测到。纯合子β地中海贫血中NK功能增强这一发现可能对评估这些患者发生恶性肿瘤的风险具有临床意义。