I型糖原贮积病是由微粒体葡萄糖-6-磷酸酶系统的葡萄糖-6-磷酸转运酶缺陷引起的。 - Suppr

Type Ib glycogen storage disease is caused by a defect in the glucose-6-phosphate translocase of the microsomal glucose-6-phosphatase system.

作者信息

Lange A J, Arion W J, Beaudet A L

出版信息

J Biol Chem. 1980 Sep 25;255(18):8381-4.

PMID:6251055

Abstract

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Type Ib glycogen storage disease is caused by a defect in the glucose-6-phosphate translocase of the microsomal glucose-6-phosphatase system.

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Type Ib glycogen storage disease is caused by a defect in the glucose-6-phosphate translocase of the microsomal glucose-6-phosphatase system.

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