Roberts J T, Byrne E H, Rosenthal D
Arch Dermatol. 1981 Jan;117(1):12-5.
Multiple fibrous histiocytomas of the dermis (dermatofibromas) were found in six males of one family. A number of the tumors fell within the histologic patterns commonly encountered in dermatofibromas, but some were unusually large and others were cytologically atypical. In addition, the proband died of a malignant fibrous histiocytoma of the lung. We believe that this is a syndrome and a familial variant of a common dermal entity.
在一个家族的6名男性中发现了真皮层多发性纤维组织细胞瘤(皮肤纤维瘤)。一些肿瘤符合皮肤纤维瘤常见的组织学模式,但有些异常大,还有一些在细胞学上不典型。此外,先证者死于肺恶性纤维组织细胞瘤。我们认为这是一种综合征,是一种常见皮肤病变的家族性变体。