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Ecto-5'-nucleotidase deficiency: association with adenosine deaminase deficiency and nonassociation with deoxyadenosine toxicity.

作者信息

Boss G R, Thompson L F, O'Connor R D, Ziering R W, Seegmiller J E

出版信息

Clin Immunol Immunopathol. 1981 Apr;19(1):1-7. doi: 10.1016/0090-1229(81)90042-8.

DOI:10.1016/0090-1229(81)90042-8
PMID:6260402
Abstract
摘要

相似文献

1
Ecto-5'-nucleotidase deficiency: association with adenosine deaminase deficiency and nonassociation with deoxyadenosine toxicity.
Clin Immunol Immunopathol. 1981 Apr;19(1):1-7. doi: 10.1016/0090-1229(81)90042-8.
2
[Primary immunodeficiencies and purine metabolism].[原发性免疫缺陷与嘌呤代谢]
Rev Clin Esp. 1985 Oct;177(6):247-53.
3
Progress in understanding the mechanism of immunodeficiency disease associated with defects in purine metabolism.嘌呤代谢缺陷相关免疫缺陷病发病机制的研究进展
Monogr Hum Genet. 1978;10:88-91. doi: 10.1159/000401572.
4
Purinogenic immunodeficiency diseases: clinical features and molecular mechanisms.嘌呤代谢异常所致免疫缺陷疾病:临床特征与分子机制
Ann Intern Med. 1980 Jun;92(6):826-31. doi: 10.7326/0003-4819-92-6-826.
5
Inherited enzyme deficiencies and immunodeficiency: adenosine deaminase (ADA) and purine nucleoside phosphorylase (PNP) deficiencies.遗传性酶缺乏症和免疫缺陷:腺苷脱氨酶(ADA)和嘌呤核苷磷酸化酶(PNP)缺乏症。
Clin Immunol Immunopathol. 1986 Jul;40(1):157-65. doi: 10.1016/0090-1229(86)90081-4.
6
Lymphospecific toxicity in adenosine deaminase deficiency and purine nucleoside phosphorylase deficiency: possible role of nucleoside kinase(s).腺苷脱氨酶缺乏症和嘌呤核苷磷酸化酶缺乏症中的淋巴细胞特异性毒性:核苷激酶的可能作用。
Proc Natl Acad Sci U S A. 1977 Dec;74(12):5677-81. doi: 10.1073/pnas.74.12.5677.
7
Adenosine deaminase and purine nucleoside phosphorylase deficiency: how they were discovered and what they may mean.腺苷脱氨酶和嘌呤核苷磷酸化酶缺乏症:它们是如何被发现的以及可能意味着什么。
Ciba Found Symp. 1978(68):3-18. doi: 10.1002/9780470720516.ch2.
8
Immunodeficiency secondary to adenosine deaminase deficiency and purine nucleoside phosphorylation deficiency.继发于腺苷脱氨酶缺乏和嘌呤核苷磷酸化酶缺乏的免疫缺陷。
Semin Hematol. 1990 Jul;27(3):260-9.
9
[Congenital immunodeficiency with adenosine deaminase and purine nucleoside phosphorylase deficiency].[伴有腺苷脱氨酶和嘌呤核苷磷酸化酶缺乏的先天性免疫缺陷]
Nihon Rinsho. 1977 Aug 10;35(8):2564-80.
10
High risk screening of adenosine deaminase and purine nucleoside phosphorylase deficiency in Japan.
Acta Paediatr Jpn. 1987 Feb;29(1):152-4. doi: 10.1111/j.1442-200x.1987.tb00022.x.

引用本文的文献

1
Further differentiation of murine double-positive thymocytes is inhibited in adenosine deaminase-deficient murine fetal thymic organ culture.在腺苷脱氨酶缺陷的小鼠胎儿胸腺器官培养中,小鼠双阳性胸腺细胞的进一步分化受到抑制。
J Immunol. 2006 May 15;176(10):5925-33. doi: 10.4049/jimmunol.176.10.5925.
2
Adenosine kinase inhibition promotes survival of fetal adenosine deaminase-deficient thymocytes by blocking dATP accumulation.腺苷激酶抑制通过阻断dATP积累促进胎儿腺苷脱氨酶缺陷胸腺细胞存活。
J Clin Invest. 2002 Aug;110(3):395-402. doi: 10.1172/JCI15683.
3
Metabolites from apoptotic thymocytes inhibit thymopoiesis in adenosine deaminase-deficient fetal thymic organ cultures.
来自凋亡胸腺细胞的代谢产物在腺苷脱氨酶缺陷型胎儿胸腺器官培养物中抑制胸腺细胞生成。
J Clin Invest. 2000 Nov;106(9):1149-57. doi: 10.1172/JCI9944.
4
B cells as well as T cells form deoxynucleotides from either deoxyadenosine or deoxyguanosine.B细胞和T细胞均可利用脱氧腺苷或脱氧鸟苷形成脱氧核苷酸。
Clin Exp Immunol. 1984 Apr;56(1):39-48.
5
Ecto-5'-nucleotidase activity in human T cell subsets. Decreased numbers of ecto-5'-nucleotidase positive cells from both OKT4+ and OKT8+ cells in patients with hypogammaglobulinemia.人T细胞亚群中的外切5'-核苷酸酶活性。低丙种球蛋白血症患者中OKT4+和OKT8+细胞中外切5'-核苷酸酶阳性细胞数量减少。
J Clin Invest. 1983 Apr;71(4):892-9. doi: 10.1172/jci110843.
6
Changes in human T lymphocytes after thymectomy and during senescence.胸腺切除术后及衰老过程中人类T淋巴细胞的变化。
J Clin Immunol. 1982 Oct;2(4):289-95. doi: 10.1007/BF00915069.
7
Adenine ribo- and deoxyribonucleotide metabolism in human erythrocytes, B- and T-lymphocyte cell lines, and monocyte-macrophages.人类红细胞、B淋巴细胞系、T淋巴细胞系及单核细胞-巨噬细胞中的腺嘌呤核糖核苷酸和脱氧核糖核苷酸代谢
Proc Natl Acad Sci U S A. 1985 Oct;82(19):6682-6. doi: 10.1073/pnas.82.19.6682.