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先天性皮肤发育不全

[Aplasia cutis congenita].

作者信息

Trevizo Ortiz L, Ruiz-Maldonado R, Tamayo s L

出版信息

Bol Med Hosp Infant Mex. 1978 Mar-Apr;35(2):333-42.

PMID:626656
Abstract

Communication of fifteen cases of Aplasia Cutis Congenita, seen from 1971 to 1977, in the Department of Pediatric Dermatology at the Hospital del Niño DIF (formerly IMAN). Patients of both sexes were equally affected. The scalp was by far the most common location of lesions. Lesiones were usually single and when multiple, they were symmetrical. The family history for the disease was negative. No relationship could be found with obstetric trauma or with the number of pregnancies. Epithelialized lesions were present in fourteen cases and ulcerated lesions in one. The more frequent congenital associated malformations were: cutaneous, neurological, ocular and osseous.

摘要

1971年至1977年期间,在国家儿童综合发展系统医院(原墨西哥营养研究所)儿科皮肤科诊治的15例先天性皮肤发育不全病例报告。男女患者受影响程度相同。头皮是迄今为止最常见的病变部位。病变通常为单发,若为多发则呈对称性分布。家族病史呈阴性,未发现与产科创伤或妊娠次数有关。14例为上皮化病变,1例为溃疡病变。较常见的先天性相关畸形有:皮肤、神经、眼部和骨骼方面的畸形。

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[Aplasia cutis congenita].先天性皮肤发育不全
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[Aplasia cutis congenita. Report of 2 cases].[先天性皮肤发育不全。2例报告]
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Aplasia cutis congenita in a defined population from northwest Spain.西班牙西北部特定人群中的先天性皮肤发育不全
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Treatment dilemma: conservative versus surgery in cutis aplasia congenita.治疗困境:先天性皮肤发育不全的保守治疗与手术治疗对比
Eur J Pediatr Surg. 2003 Apr;13(2):125-9. doi: 10.1055/s-2003-39562.
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[Aplasia cutis congenita: surgical treatment and results in 36 cases].[先天性皮肤发育不全:36例手术治疗及结果]
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[Aplasia cutis circumscripta congenita].先天性局限性皮肤发育不全
Wien Med Wochenschr. 1977 Jun 20;127(12):406-8.
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[Aplasia cutis congenita in a newborn: etiopathogenic review and diagnostic approach].[新生儿先天性皮肤发育不全:病因学综述与诊断方法]
An Esp Pediatr. 2000 May;52(5):453-6.
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Extraordinary aplasia cutis congenita, or a new entity?罕见的先天性皮肤发育不全,还是一种新的疾病实体?
Helv Paediatr Acta. 1981 Jul;36(3):281-5.
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Cutis marmorata telangiectatica congenita: a prospective study of 27 cases and review of the literature with proposal of diagnostic criteria.先天性大理石样皮肤血管扩张症:27例前瞻性研究及文献复习并提出诊断标准
Clin Exp Dermatol. 2009 Apr;34(3):319-23. doi: 10.1111/j.1365-2230.2008.03074.x. Epub 2009 Jan 12.

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Aplasia cutis congenita: Two case reports and discussion of the literature.先天性皮肤发育不全:两例病例报告及文献讨论
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