杜兴氏肌营养不良症和肌强直中红细胞影（钠+钾）ATP酶活性
Erythrocyte ghosts (Na+ + K+) ATPase activity in Duchenne's dystrophy and myotonia.
作者信息
Niebrój-Dobosz I
出版信息
J Neurol. 1976 Nov 26;214(1):61-9. doi: 10.1007/BF00313489.
PMID:62828
Abstract
In Duchenne muscular dystrophy the activity of (Na+ + K+)ATPase in erythrocyte ghosts is reduced and its reaction to ouabain is paradoxical both in low sodium and high sodium systems. No such changes were seen in a case of Becker dystrophy, in limb-girdle dystrophy, and in neurogenic atrophy of muscles. In myotonic dystrophy and congenital myotonia the activity of ATPase and its inhibition by ouabain were depressed.
摘要
在杜兴氏肌营养不良症中，红细胞膜空壳中（钠+钾）ATP酶的活性降低，并且在低钠和高钠系统中其对哇巴因的反应是反常的。在贝克肌营养不良症、肢带型肌营养不良症和肌肉神经源性萎缩病例中未观察到此类变化。在强直性肌营养不良症和先天性肌强直中，ATP酶的活性及其被哇巴因的抑制作用均降低。
相似文献
1
Erythrocyte ghosts (Na+ + K+) ATPase activity in Duchenne's dystrophy and myotonia.杜兴氏肌营养不良症和肌强直中红细胞影（钠+钾）ATP酶活性
J Neurol. 1976 Nov 26;214(1):61-9. doi: 10.1007/BF00313489.
2
Adenylate cyclase and ATPase activities in red cell membranes of patients and genetic carriers of Duchenne muscular dystrophy.
Clin Chim Acta. 1979 Sep 3;96(3):255-9. doi: 10.1016/0009-8981(79)90436-4.
3
(Na++K+)-ATPase of Duchenne muscular dystrophy erythrocyte ghosts.
Life Sci. 1978 Jan;22(1):127-32. doi: 10.1016/0024-3205(78)90420-4.
4
Erythrocyte membrane abnormalities in human myotonic dystrophy.
J Neurol Sci. 1980 Jun;46(3):333-40. doi: 10.1016/0022-510x(80)90058-1.
5
Erythrocyte flexibility, ATPase activities and Ca efflux in patients with Duchenne muscular dystrophy, myotonic muscular dystrophy and congenital myotonia.
J Neurol Sci. 1983 Mar;58(3):399-407. doi: 10.1016/0022-510x(83)90098-9.
6
Effect of ouabain upon erythrocyte membrane adenosine triphosphatase in Duchenne muscular dystrophy.
J Neurol Sci. 1977 Dec;34(3):365-72. doi: 10.1016/0022-510x(77)90153-8.
7
The effect of ouabain on erythrocyte adenosine triphosphatase activity in relation to cell age in vivo and Duchenne muscular dystrophy.
Biochem Soc Trans. 1980 Dec;8(6):718. doi: 10.1042/bst0080718.
8
Na+ + K+ ATPase of erythrocyte membranes in Duchenne muscular dystrophy.
Neurology. 1981 Mar;31(3):293-7. doi: 10.1212/wnl.31.3.293.
9
[Adenosine triphosphatase activities of the erythrocyte membrane in Duchenne's myodystrophy].
Pediatriia. 1981 May(5):34-5.
10
The sodium pump of erythrocytes from patients with Duchenne muscular dystrophy: effect of ouabain on the active sodium flux and on (Na+, K+)ATPase.杜兴氏肌营养不良症患者红细胞的钠泵：哇巴因对活性钠通量和（钠，钾）ATP酶的影响。
J Neurol. 1978 Mar 9;217(4):287-94. doi: 10.1007/BF00312990.
引用本文的文献
1
Duchenne muscular dystrophy: pathogenetic aspects and genetic prevention.杜氏肌营养不良症：发病机制及基因预防
Hum Genet. 1984;66(1):17-40. doi: 10.1007/BF00275183.
2
The sodium pump of erythrocytes from patients with Duchenne muscular dystrophy: effect of ouabain on the active sodium flux and on (Na+, K+)ATPase.杜兴氏肌营养不良症患者红细胞的钠泵：哇巴因对活性钠通量和（钠，钾）ATP酶的影响。
J Neurol. 1978 Mar 9;217(4):287-94. doi: 10.1007/BF00312990.
3
Erythrocyte ghost (Na+ + K+) ATPase activity in mice with hereditary muscular dystrophy (strain C57 BL/64J/dy).遗传性肌营养不良小鼠（C57 BL/64J/dy品系）的红细胞影（Na+ + K+）ATP酶活性
J Neurol. 1978 Feb 14;217(3):183-9. doi: 10.1007/BF00312959.
本文引用的文献
1
Protein measurement with the Folin phenol reagent.使用福林酚试剂进行蛋白质测定。
J Biol Chem. 1951 Nov;193(1):265-75.
2
ENZYMATIC BASIS FOR ACTIVE TRANSPORT OF NA+ AND K+ ACROSS CELL MEMBRANE.钠离子和钾离子跨细胞膜主动运输的酶学基础
Physiol Rev. 1965 Jul;45:596-617. doi: 10.1152/physrev.1965.45.3.596.
3
AN ENZYMATIC MECHANISM OF ACTIVE SODIUM AND POTASSIUM TRANSPORT.主动钠钾转运的一种酶促机制。
J Histochem Cytochem. 1965 Feb;13:105-12. doi: 10.1177/13.2.105.
4
PHOSPHOLIPID REQUIREMENT OF NA+,K+-ACTIVATED ADENOSINE TRIPHOSPHATASE FROM RAT BRAIN.大鼠脑钠钾激活三磷酸腺苷酶的磷脂需求
Arch Biochem Biophys. 1964 Oct;108:47-52. doi: 10.1016/0003-9861(64)90353-4.
5
BIPHASIC RENAL EFFECTS OF OUABAIN IN THE CHICKEN: CORRELATION WITH A MICROSOMAL NA+-K+ STIMULATED ATP-ASE.哇巴因对鸡的双相性肾脏效应：与微粒体钠钾激活ATP酶的相关性
J Pharmacol Exp Ther. 1964 Oct;146:92-8.
6
Lipoprotein nature of red cell adenosine triphosphatase.红细胞三磷酸腺苷酶的脂蛋白性质
Nature. 1962 Nov 17;196:677. doi: 10.1038/196677a0.
7
Cation transport and structure of the red-cell plasma membrane.红细胞质膜的阳离子转运与结构
Circulation. 1962 Nov;26:1202-13. doi: 10.1161/01.cir.26.5.1201.
8
Erythrocyte electrolytes in muscle disease.肌肉疾病中的红细胞电解质
J Lab Clin Med. 1959 Dec;54:867-70.
9
Adenosinetriphosphatase activity and the active movements of alkali metal ions.三磷酸腺苷酶活性与碱金属离子的主动转运
J Physiol. 1961 Apr;156(2):274-93. doi: 10.1113/jphysiol.1961.sp006675.
10
Serum enzymes in the physiopathology of muscle.肌肉生理病理学中的血清酶。
Ann N Y Acad Sci. 1958 Oct 13;75(1):235-49. doi: 10.1111/j.1749-6632.1958.tb36870.x.
Zotero 插件