Harms D
Klin Padiatr. 1982 Jul-Aug;194(4):275-80. doi: 10.1055/s-2008-1033817.
Until April 1981 malignant soft tissue sarcomas were registered from 238 patients. Rhabdomyosarcoma was the most common tumor (115/238 = 48.3%). The embryonal subtype was predominantly seen among the rhabdomyosarcomas (83/115 = 72.2%). Rhabdomyosarcomas were localized most frequently in the head and neck area (40/115 = 34.8%), followed by genitourinary system (15/115), pelvis soft tissue (12), abdomen (10) and extremities (10). Non-rhabdomyosarcomatous soft tissue sarcomas (123/238 = 51.7%) were synovial sarcomas (20 = 8.4%), fibrosarcomas including spindle cell sarcoma (17 = 7.4%), leiomyosarcomas (12 = 5.0%), malignant tumors of the vascular system (11 = 4.6%) and neurofibrosarcomas (9 = 3.8%). Other types of sarcoma were extremely rare. 42 (17.6%) of all soft tissue sarcomas could not be classified histogenetically. Rhabdomyosarcomas could be diagnosed much more accurately (105/115 = 91.3%), compared to all other soft tissue sarcomas (99/121 = 81.8%). At present, the most difficult diagnostic problems remain with the tumors of connective tissue, in particular with fibrosarcomas and with the differential diagnosis of juvenile fibrosarcomas versus juvenile fibromatoses.
截至1981年4月，共登记了238例恶性软组织肉瘤患者。横纹肌肉瘤是最常见的肿瘤（115/238 = 48.3%）。胚胎型亚型在横纹肌肉瘤中最为常见（83/115 = 72.2%）。横纹肌肉瘤最常发生于头颈部（40/115 = 34.8%），其次是泌尿生殖系统（15/115）、盆腔软组织（12例）、腹部（10例）和四肢（10例）。非横纹肌肉瘤性软组织肉瘤（123/238 = 51.7%）包括滑膜肉瘤（20例 = 8.4%）、纤维肉瘤（包括梭形细胞肉瘤，17例 = 7.4%）、平滑肌肉瘤（12例 = 5.0%）、血管系统恶性肿瘤（11例 = 4.6%）和神经纤维肉瘤（9例 = 3.8%）。其他类型的肉瘤极为罕见。所有软组织肉瘤中有42例（17.6%）无法进行组织学分类。与所有其他软组织肉瘤（99/121 = 81.8%）相比，横纹肌肉瘤的诊断准确性更高（105/115 = 91.3%）。目前，结缔组织肿瘤，尤其是纤维肉瘤以及幼年型纤维肉瘤与幼年型纤维瘤病的鉴别诊断仍然是最困难的诊断问题。
