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下肢不成比例生长。特纳综合征身材矮小的一个主要决定因素。

Disproportionate growth of the lower extremities. A major determinant of short stature in Turner's syndrome.

作者信息

Neufeld N D, Lippe B M, Kaplan S A

出版信息

Am J Dis Child. 1978 Mar;132(3):296-8. doi: 10.1001/archpedi.1978.02120280080018.

DOI:10.1001/archpedi.1978.02120280080018
PMID:629248
Abstract

The relationships between the height (H), sitting height (SH), and the lower segment (H-SH) were studied in a group of 21 patients with Turner's syndrome. The SH/H ratio was markedly abnormal (0.55), equivalent to that of 6-year-old normal girls. The abnormality in ratio was a result of markedly shortened lower extremities. Further, there was a significant inverse correlation between SH/H-SH ratio and height such that patients with the most shortening of their legs were the shortest. The degree of abnormality in lower segment, therefore, is a major determinant of stature in Turner's syndrome.

摘要

对一组21例特纳综合征患者的身高(H)、坐高(SH)以及下肢长度(H - SH)之间的关系进行了研究。坐高与身高之比(SH/H)明显异常(0.55),与6岁正常女孩相当。该比例异常是下肢明显缩短所致。此外,SH/H - SH比值与身高之间存在显著负相关,即腿部缩短最明显的患者身高最矮。因此,下肢的异常程度是特纳综合征患者身高的主要决定因素。

相似文献

1
Disproportionate growth of the lower extremities. A major determinant of short stature in Turner's syndrome.下肢不成比例生长。特纳综合征身材矮小的一个主要决定因素。
Am J Dis Child. 1978 Mar;132(3):296-8. doi: 10.1001/archpedi.1978.02120280080018.
2
Body proportions in Turner's syndrome.特纳综合征的身体比例
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Decreased metabolic clearance of endogenous growth hormone and specific alterations in the pulsatile mode of growth hormone secretion occur in prepubertal girls with Turner's syndrome. Genentech Collaborative Group.患有特纳综合征的青春期前女孩体内,内源性生长激素的代谢清除率降低,且生长激素分泌的脉冲模式出现特定改变。基因泰克协作组。
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[Turner's syndrome: subjects with a normal body mass at birth grow taller than born small for gestational age].特纳综合征:出生时体重正常的患者比出生时小于胎龄儿长得更高。
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Leg length, body proportion, and health: a review with a note on beauty.腿长、身体比例与健康:综述及对美的注脚。
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Effects of growth hormone on body proportions in Turner syndrome compared with non-treated patients and normal women.
生长激素对特纳综合征患者与未治疗患者和正常女性身体比例的影响。
J Endocrinol Invest. 2010 Nov;33(10):691-5. doi: 10.1007/BF03346671. Epub 2010 Mar 30.
4
Body proportions in individuals with Turner syndrome. The Dutch Growth Hormone Working Group.
Eur J Pediatr. 1993 Oct;152(10):813-7. doi: 10.1007/BF02073377.
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Body proportions in Turner's syndrome.特纳综合征的身体比例
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