Chahinian A P, Kirschner P A, Dikman S H, Rammos K S, Holland J F
Arch Intern Med. 1983 Jul;143(7):1462-4.
The diagnosis of Carney's triad requires the coexistence of at least two of three rare disorders, including gastric epithelioid leiomyosarcoma, pulmonary chondroma, and functioning extra-adrenal paraganglioma. Seventeen cases have been reported so far, occurring predominantly in young female patients. We report herein the 18th case of this entity and the first case, to our knowledge, where pulmonary metastases from a gastric leiomyosarcoma coexisted in a patient with benign pulmonary chondromas.
卡尼三联征的诊断需要三种罕见疾病中的至少两种同时存在,这三种疾病包括胃上皮样平滑肌肉瘤、肺软骨瘤和功能性肾上腺外副神经节瘤。迄今为止,已报告了17例病例,主要发生在年轻女性患者中。在此,我们报告该疾病的第18例病例,据我们所知,这是首例胃平滑肌肉瘤肺转移与良性肺软骨瘤并存的病例。