Pernot C, Worms A M, Henry M, Marçon F, Weber J L
Sem Hop. 1983 May 26;59(21):1591-6.
The authors report four cases of fistulae between coronary arteries and the main pulmonary artery or its branches. Proximal fistulae, often considered with coronary-cardiac fistulae (between coronary arteries and cardiac cavities, usually in the right heart) probably result from accessory coronary buds originating in the truncus arteriosus, on its pulmonary part, as in anomalous coronary arteries stemming from the pulmonary trunk. Two such cases are reported, including one in a girl with severe congenital mitral insufficiency. Peripheral fistulae probably do not result from a single mechanism, and their congenital or acquired origin is often difficult to determine, especially in adults. Nevertheless, in a 54-year-old female with angina by coronary steal, without any associated pulmonary disease, the fistula is probably congenital. On the other hand, in a boy who had a Blalock operation for Tetralogy of Fallot, the fistula is probably acquired, as part of the collateral circulation which developed after pleuro-pericardial symphysis. Such fistulae usually do not require surgery except in cases of coronary artery steal, which are exceptional in children but not infrequent in adults.
作者报告了4例冠状动脉与主肺动脉或其分支之间的瘘管病例。近端瘘管常被认为与冠状-心内瘘管(冠状动脉与心腔之间的瘘管,通常位于右心)有关,可能源于起源于动脉干肺部分的副冠状动脉芽,就像起源于肺动脉干的异常冠状动脉一样。本文报告了2例此类病例,其中1例为患有严重先天性二尖瓣关闭不全的女孩。周围性瘘管可能并非由单一机制引起,其先天性或后天性起源往往难以确定,尤其是在成年人中。然而,在一名因冠状动脉窃血而患心绞痛且无任何相关肺部疾病的54岁女性中,瘘管可能是先天性的。另一方面,在一名因法洛四联症接受布莱洛克手术的男孩中,瘘管可能是后天获得的,是胸膜心包粘连后形成的侧支循环的一部分。除冠状动脉窃血情况外,此类瘘管通常不需要手术,冠状动脉窃血在儿童中较为罕见,但在成年人中并不少见。