Selective ACTH insensitivity, achalasia, and alacrima: a multisystem disorder presenting in childhood.

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作者信息

Geffner M E, Lippe B M, Kaplan S A, Berquist W E, Bateman J B, Paterno V I, Seegan R

出版信息

Pediatr Res. 1983 Jul;17(7):532-6. doi: 10.1203/00006450-198307000-00003.

DOI:10.1203/00006450-198307000-00003

PMID:6312400

Abstract

摘要

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Selective ACTH insensitivity, achalasia, and alacrima: a multisystem disorder presenting in childhood.

Pediatr Res. 1983 Jul;17(7):532-6. doi: 10.1203/00006450-198307000-00003.

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[Simultaneous occurrence of selective ACTH deficiency , achalasia, alacrimia and hyperlipoproteinemia].[选择性促肾上腺皮质激素缺乏、贲门失弛缓症、无泪症和高脂蛋白血症同时发生]

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Association of adult achalasia and alacrima.成人贲门失弛缓症与无泪症的关联。

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Neurological and adrenal dysfunction in the adrenal insufficiency/alacrima/achalasia (3A) syndrome.肾上腺功能不全/无泪/贲门失弛缓症（3A）综合征中的神经和肾上腺功能障碍。

Arch Dis Child. 1993 Jun;68(6):779-82. doi: 10.1136/adc.68.6.779.

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