Condamine J L, Louis B, Richter D, Roffe J L, Aubriot J H
Sem Hop. 1984 Mar 8;60(11):780-3.
The authors present two cases of epithelioid sarcoma of the hand and one of the foot with clinical interest. This recently described tumor (Enzinger, 1970), is relatively rare. It occurs in the hand, forearm, pretibial region and foot and affects principally young adults. It should be emphasized, and this is borne out in the literature, that this tumor may appear perfectly benign and often has a course of long duration. The difficulty of clinical and especially of histologic diagnosis as well as the difficulty of determining the boundaries of extension of the tumor make it necessary to carry out radical surgery (amputation or rarely block excision). Every author agrees that local excision is to be condemned, there being an 85% recurrence rate. Spread of the tumor is by way of the fascial planes and tendon sheaths. Lymphatic and pulmonary metastases occur particularly when there is vascular invasion.
作者报告了两例手部和一例足部上皮样肉瘤病例,具有临床研究价值。这种最近才被描述的肿瘤(恩津格,1970年)相对罕见。它发生于手部、前臂、胫前区和足部,主要影响年轻人。应当强调的是,文献也证实了这一点,即这种肿瘤可能看似完全良性,且病程往往很长。临床诊断尤其是组织学诊断的困难,以及确定肿瘤扩展边界的困难,使得有必要进行根治性手术(截肢,很少进行整块切除)。每位作者都认为局部切除是不可取的,因为复发率高达85%。肿瘤通过筋膜平面和腱鞘扩散。特别是当有血管侵犯时,会发生淋巴转移和肺转移。