Roth E F, Raventos-Suarez C, Rinaldi A, Nagel R L
Proc Natl Acad Sci U S A. 1983 Jan;80(1):298-9. doi: 10.1073/pnas.80.1.298.
Glucose-6-phosphate dehydrogenase (G6PD; EC 1.1.1.49)-deficient red blood cells from male hemizygotes and female heterozygotes from the island of Sardinia were studied for their ability to support growth in vitro of the malaria-causing organism Plasmodium falciparum. Parasite growth was approximately one-third of normal in both hemi- and heterozygotes for G6PD deficiency. In Sardinians with the beta 0-thalassemia trait, parasite growth was normal except when G6PD deficiency occurred together with the thalassemia trait. The data support the hypothesis that G6PD deficiency may confer a selective advantage in a malarious area; the female heterozygote may be at a particular advantage because resistance to malaria equals that of male hemizygotes, but the risk of fatal hemolysis may be less. However, more female heterozygotes must be studied to confirm this hypothesis. No protective effect of beta 0-thalassemia trait could be demonstrated in vitro.
对来自撒丁岛的男性半合子和女性杂合子的葡萄糖-6-磷酸脱氢酶(G6PD;EC 1.1.1.49)缺乏的红细胞进行了研究,以观察它们支持疟原虫恶性疟原虫体外生长的能力。对于G6PD缺乏的半合子和杂合子,寄生虫生长约为正常水平的三分之一。在具有β0地中海贫血特征的撒丁岛人中,除了G6PD缺乏与地中海贫血特征同时出现外,寄生虫生长正常。这些数据支持了这样一种假设,即G6PD缺乏可能在疟疾流行地区赋予一种选择优势;女性杂合子可能具有特殊优势,因为对疟疾的抵抗力与男性半合子相同,但致命溶血的风险可能较小。然而,必须研究更多的女性杂合子以证实这一假设。在体外未证明β0地中海贫血特征有保护作用。