Muntean W, Kaspar G, Stöffler G, Petek W
Padiatr Padol. 1978;13(2):205-10.
The investigation of a girl aged 8 with hereditary hemorrhagic telangiectasia showed an abnormality of primary hemostasis. The bleeding time was at the upper end of normal and platelet adhesiveness was decreased to a variable extent. Platelet life span was shortened, presumably due to the telangiectatic lesions typical of this disease. Platelet aggregation and ADP-content were normal as was the plasma coagulation system.
对一名8岁遗传性出血性毛细血管扩张症女孩的调查显示,其初级止血功能存在异常。出血时间处于正常范围上限,血小板黏附性不同程度降低。血小板寿命缩短,推测是由于该病典型的毛细血管扩张性病变所致。血小板聚集和ADP含量正常,血浆凝血系统也正常。