Nagao T, Shigenobu M, Teramoto S, Fukuda K, Mizushima M, Nishioka S, Mizuta T, Kojo T
Gan No Rinsho. 1984 Jul;30(8):968-74.
A 23-year-old man with Von Recklinghausen's disease was admitted because of abdominal pain. The preoperative diagnosis was malignant mesenteric tumor. Laparotomy was done and the tumor was located in the mesentery of the ileum which showed numerous tortuous cords or bulbous projections from the surface. Partial resection of the involved ileum and the mesentery was performed. Histological examination revealed plexiform neurofibroma and malignant Schwannoma of the mesentery. It is very difficult to preoperatively diagnose early associated lesions of Von Recklinghausen's disease. Therefore, careful examination of the GI tract is important so that earlier therapy can be carried out.
一名患有冯雷克林霍增氏病的23岁男性因腹痛入院。术前诊断为肠系膜恶性肿瘤。进行了剖腹手术，肿瘤位于回肠系膜，表面可见许多迂曲的索条或球状突起。对受累的回肠和肠系膜进行了部分切除。组织学检查显示为肠系膜丛状神经纤维瘤和恶性施万细胞瘤。术前诊断冯雷克林霍增氏病早期相关病变非常困难。因此，仔细检查胃肠道很重要，以便能更早地进行治疗。
