Touboul A, Legendre T, Magnier S, Casasoprana A, Vernant P
Arch Mal Coeur Vaiss. 1984 Dec;77(13):1547-50.
Idiopathic right atrial dilatation is a rare and probably congenital malformation. Two new cases are reported, in an 18 months old infant and a six week old baby, both presenting with supraventricular tachyarrhythmias. Clinical examination was normal. Chest X-ray showed bulging of the right heart border and electrocardiography revealed partial right bundle branch block. The diagnosis was made by echocardiography which showed aneurysmal dilatation of the right atrium. There were no signs of valvular heart disease or of an intracardiac shunt; the septal tricuspid leaflet was in its normal position. M-mode recordings showed no signs of Ebstein's anomaly. The diagnosis was confirmed by cardiac catheterisation in the first case; this investigation seemed to be pointless in the second case. Both children experienced many episodes of supraventricular tachyarrhythmias. The first developed tricuspid regurgitation but the second remains asymptomatic.
特发性右心房扩张是一种罕见的、可能为先天性的畸形。本文报告了两例新病例,一例为18个月大的婴儿,另一例为6周大的婴儿,二者均表现为室上性快速性心律失常。临床检查正常。胸部X线显示右心缘膨隆,心电图显示不完全性右束支传导阻滞。诊断通过超声心动图做出,显示右心房呈瘤样扩张。未发现瓣膜性心脏病或心内分流的迹象;三尖瓣隔叶位置正常。M型记录未显示埃布斯坦畸形的迹象。第一例通过心导管检查确诊;第二例进行此项检查似乎没有意义。两个孩子都经历了多次室上性快速性心律失常发作。第一个孩子出现了三尖瓣反流,但第二个孩子仍无症状。