Gilbert R F, Waugh D E, Clarke J S
South Med J. 1978 May;71(5):530-2. doi: 10.1097/00007611-197805000-00015.
A surgically treated case of a mesenchymal hamartoma, a rare, benign liver tumor of infants and occasionally children, is reported. The clinical picture is characterized by marked, usually rapid abdominal enlargement. If untreated, the tumor may compromise other organ systems, resulting in death. The treatment is surgical removal. The tumor is characterized by proliferation of collagenous connective tissue, immature mesenchyme, and multiple cysts or pseudocysts of varying sizes. The origin of the tumor has not yet been definitely determined. Ultrasonography combined with radionuclide scanning was useful in establishing a working, preoperative diagnosis.
本文报道了一例经手术治疗的间叶性错构瘤病例，这是一种罕见的婴幼儿及偶尔发生于儿童的肝脏良性肿瘤。临床表现以明显且通常迅速的腹部膨隆为特征。若不治疗，肿瘤可能会影响其他器官系统，导致死亡。治疗方法为手术切除。该肿瘤的特征是胶原结缔组织、未成熟间充质以及大小各异的多个囊肿或假囊肿增生。肿瘤的起源尚未明确确定。超声检查联合放射性核素扫描有助于做出有效的术前诊断。
