Horita N, Ishii T, Izumiyama Y
Acta Neuropathol. 1980;49(1):19-27. doi: 10.1007/BF00692215.
Lesions in the CNS induced by 6-aminonicotinamide (6-AN) presented a spongy state of the gray matter and neuronal chromatolysis. With aging of the experimental animals the lesions extended from the phylogenetically early developed structures to those developed later, i.e., from spinal gray matter, dentate nuclei, and brain stem nuclei through limbic structures and striatum to the cerebral cortex. Changes of the neurons were more prominent with aging. Lesions in the CNS of rats at the age, corresponding to the involutional period in the human, were similar to those of Creutzfeldt-Jakob disease (C-J) disease) in the presenile age. In recent years, the resemblance between C-J disease and pellagra encephalopathy had been noted by several authors, and they resemble the lesions caused by 6-AN, an antimetabolite of nicotinamide used in our experiment. This evidence, therefore, has led to the hypothesis that dysfunction of NAD(H)- or NADP(H)-dependent enzymes in the CNS of the aged, even if not the primary cause, may be one possible pathogenetic factor of C-J disease.
6-氨基烟酰胺(6-AN)诱导的中枢神经系统病变呈现出灰质的海绵状状态和神经元染色质溶解。随着实验动物的衰老,病变从系统发育早期发育的结构扩展到后期发育的结构,即从脊髓灰质、齿状核和脑干核,通过边缘结构和纹状体扩展到大脑皮层。随着衰老,神经元的变化更加明显。处于相当于人类 involutional 期年龄的大鼠中枢神经系统病变与早老性克雅氏病(C-J 病)的病变相似。近年来,几位作者注意到 C-J 病与糙皮病脑病之间的相似性,并且它们类似于我们实验中使用的烟酰胺抗代谢物 6-AN 所引起的病变。因此,这一证据导致了这样一种假设,即老年人中枢神经系统中依赖 NAD(H) 或 NADP(H) 的酶功能障碍,即使不是主要原因,也可能是 C-J 病的一种可能致病因素。