Rautenburg H W, Askevold I B
Herz. 1980 Oct;5(5):306-13.
Of 89 children with angiographically-documented pulmonic stenosis and intact ventricular septum (PST), 76 (85.4%) had valvular, 11 (12.4%) infundibular and 2 (2%) had supravalvular lesions. Standard, p. a. view, chest X-rays of children with a mean age of 6 7/12 years were evaluated with respect to 1. cardiac enlargement; 2. prominence of the pulmonic trunk; 3. diminished pulmonary vascular markings. The patients were divided into 3 groups according to the gradient measured across the pulmonic valve: Group 1: systolic pressure gradient less than 30 mm Hg (mild PST), 28 children; group 2: systolic pressure gradient between 30 and 80 mm Hg (moderate PST), 37 children; group 3: systolic pressure gradient greater than 80 mm Hg (severe PST), 24 children. Cardiac enlargement was found in a total of 56.2% of the children with no statistical difference in the severity of the lesion. A markedly ectatic pulmonary segment was observed in 12.5% of the children in group 3 but only in 2.7% of those in groups 1 and 2 respectively. Diminished pulmonary vascular markings were observed in a total of 9% with a distribution including no patient in group 1, 10.8% in group 2 and 16.6% in group 3. On combining all three of the radiologic criteria, 9% demonstrated completely normal findings of the heart and lungs, 5.6% showed cardiac enlargement with marked prominence of the pulmonic trunk and diminished pulmonary vascular markings. In the remaining patients, no statistically significant relationship between the constellation of findings and the severity of the stenosis was found. Thus, the results show that, in the individual case, the diagnosis of pulmonic stenosis with intact ventricular septum cannot be established from the standard chest X-ray.
在89例经血管造影证实为肺动脉狭窄且室间隔完整(PST)的儿童中,76例(85.4%)为瓣膜型,11例(12.4%)为漏斗部型,2例(2%)为瓣膜上型病变。对平均年龄为6又7/12岁儿童的标准正位胸部X线片进行了评估,涉及以下方面:1. 心脏扩大;2. 肺动脉主干突出;3. 肺血管纹理减少。根据经肺动脉瓣测量的压力阶差,将患者分为3组:第1组:收缩压阶差小于30 mmHg(轻度PST),28例儿童;第2组:收缩压阶差在30至80 mmHg之间(中度PST),37例儿童;第3组:收缩压阶差大于80 mmHg(重度PST),24例儿童。总共56.2%的儿童存在心脏扩大,病变严重程度方面无统计学差异。第3组中12.5%的儿童观察到明显扩张的肺段,而第1组和第2组分别仅为2.7%。总共9%的儿童观察到肺血管纹理减少,分布情况为第1组无患者,第2组为10.8%,第3组为16.6%。综合所有三项放射学标准,9%的儿童心肺表现完全正常,5.6%表现为心脏扩大伴肺动脉主干明显突出及肺血管纹理减少。在其余患者中,未发现检查结果组合与狭窄严重程度之间存在统计学显著关系。因此,结果表明,对于个别病例,不能根据标准胸部X线片确诊室间隔完整的肺动脉狭窄。