肠淋巴管扩张症——两例中国儿童病例报告

Intestinal lymphangiectasia--a report in two Chinese children.

作者信息

Quak S H, Wee A, Yap H K, Tay J S, Quah T C, Yip W C

出版信息

Aust Paediatr J. 1984 May;20(2):151-3. doi: 10.1111/j.1440-1754.1984.tb00066.x.

DOI:10.1111/j.1440-1754.1984.tb00066.x

Abstract

Two Chinese infants with asymmetrical lymphoedema and steatorrhoea were investigated. The laboratory investigations showed that they had hypoproteinaemia without proteinuria. One of them showed peripheral lymphopenia and hypogammaglobulinaemia. Radiologically, they had evidence of extensive lymphangiectasia of the small intestine. This was confirmed histologically. Endoscopy of one of them showed diffuse milky nodular duodenal mucosa. The appearance of the mucosa was rather typical of intestinal lymphangiectasia.

摘要

对两名患有不对称性淋巴水肿和脂肪泻的中国婴儿进行了调查。实验室检查显示他们有低蛋白血症但无蛋白尿。其中一名婴儿表现为外周淋巴细胞减少和低丙种球蛋白血症。放射学检查显示他们有小肠广泛淋巴管扩张的证据，这一点通过组织学检查得以证实。对其中一名婴儿进行的内镜检查显示十二指肠黏膜弥漫性呈乳状结节。黏膜外观颇具肠道淋巴管扩张的典型特征。