Vatti M, Giordano A, Giordano M
Z Rheumatol. 1984 Jul-Aug;43(4):171-4.
120 patients with progressive systemic sclerosis (PSS) were studied and subdivided into five groups according to the PSS classification of Giordano et al. ("acute diffuse scleroderma", "intermediate syndrome", "acrosclerosis sensu stricto", "sclerodactylia" and "sclerosis sine scleroderma"). In all five subgroups telangiectasias incidence was high (from 75% to 100%). The "ramosus" and "telangiectatic mats" types occur more frequently than other forms of telangiectasias. The former particularly involves the face, neck and chest; whereas the latter more usually involves the upper extremities and is the only type which appears at the lips. Cuticular telangiectasia is a third type, as important as the others but less frequent. The incidence of telangiectasias is related to disease duration. Similar telangiectasias have been observed in rarer patients with other connective tissue diseases (SLE, RA, dermatomyositis and undifferentiated connective tissue diseases).
对120例进行性系统性硬化症(PSS)患者进行了研究,并根据Giordano等人的PSS分类(“急性弥漫性硬皮病”、“中间综合征”、“严格意义上的肢端硬化症”、“硬皮病指”和“无硬皮病的硬化症”)将其分为五组。在所有五个亚组中,毛细血管扩张的发生率都很高(从75%到100%)。“树枝状”和“毛细血管扩张性斑片”类型比其他形式的毛细血管扩张更常见。前者尤其累及面部、颈部和胸部;而后者更常累及上肢,并且是唯一出现在嘴唇上的类型。表皮毛细血管扩张是第三种类型,与其他类型同样重要,但较少见。毛细血管扩张的发生率与病程有关。在患有其他结缔组织疾病(系统性红斑狼疮、类风湿关节炎、皮肌炎和未分化结缔组织疾病)的罕见患者中也观察到了类似的毛细血管扩张。