Herron L D, Westin G W, Dawson E G
J Bone Joint Surg Am. 1978 Apr;60(3):293-9.
Scoliosis was evident in eighteen of eighty-eight patients with arthrogryposis multiplex congenita. The predominant pattern of spinal deformity was a structural thoracolumbar double curve that extended to the sacrum and was associated with pelvic obliquity and lumbar hyperlordosis. Significant contractures about the hips, dislocation of the hip, or both were present in all patients but one. Most of the curves were progressive and they became rigid and fixed at an early age. There was progression of the pelvic obliquity coincident with progression of the curve. Treatment by corrective casts or a Milwaukee brace was ineffective and if surgical treatment directed at the pelvic obliquity did not correct that deformity, spine fusion to the sacrum appeared necessary.
在88例先天性多发性关节挛缩症患者中，18例存在脊柱侧弯。脊柱畸形的主要类型是结构性胸腰段双弯，延伸至骶骨，并伴有骨盆倾斜和腰椎前凸增加。除1例患者外，所有患者均存在明显的髋关节挛缩、髋关节脱位或两者兼有。大多数侧弯呈进行性发展，且在早期就变得僵硬和固定。骨盆倾斜度随着侧弯的进展而加重。使用矫正支具或密尔沃基支具治疗无效，若针对骨盆倾斜的手术治疗无法纠正该畸形，则似乎有必要进行脊柱至骶骨的融合手术。
