Balducci G, Mautone A, Pintucci R, Loverro G, Caruso G, Amendola F
Pediatr Med Chir. 1984 Jul-Aug;6(4):543-7.
Two cases of congestive heart failure in utero with fetal hydrops are reported. The diagnosis was made during pregnancy by means of echography. Cardiac failure, derived from supraventricular tachycardia not associated with structural anomalies of the heart, was observed in one of the patients. By digoxin administration and vagal stimulation the rhythm reverted to sinus, one hour after birth. In the second case fetal echography showed a fetus with serious bradycardia (45/min.) and ascites. On the bases of a median located and symmetric liver and of a complex heart malformation a diagnosis of "isomeric syndrome" was supposed. One hour after vaginal delivery, the newborn dead and autopsy confirmed a left isomeric syndrome with polisplenia and complex congenital cardiopathy (left ventricle and mitral hypoplasy, double outlet right ventricle, pulmonary stenosis, anomalous systemic and pulmonary venous return).
报告了两例宫内充血性心力衰竭伴胎儿水肿的病例。诊断在孕期通过超声检查做出。其中一名患者观察到由与心脏结构异常无关的室上性心动过速引起的心力衰竭。通过给予地高辛和迷走神经刺激，出生后一小时心律恢复为窦性。在第二例中，胎儿超声检查显示胎儿严重心动过缓（45次/分钟）并伴有腹水。基于肝脏位于中线且对称以及复杂的心脏畸形，推测诊断为“异构综合征”。阴道分娩后一小时，新生儿死亡，尸检证实为左异构综合征伴多脾和复杂先天性心脏病（左心室和二尖瓣发育不全、右心室双出口、肺动脉狭窄、体循环和肺静脉异常回流）。
