双侧先天性硬膜下囊肿伴脑穿通畸形和脑脊液-硬膜下瘘。两例报告。

Bilateral congenital subdural cysts associated with porencephaly and CSF-subdural fistula. A report of two cases.

作者信息

Agamanolis D P, Robinson H B, Jacobs I B, Graulich K

出版信息

Arch Neurol. 1978 Jun;35(6):370-6. doi: 10.1001/archneur.1978.00500300044008.

DOI:10.1001/archneur.1978.00500300044008

Abstract

Tow infants had bilateral congenital subdural cysts associated with encephaloclastic porencephaly and a CSF-subdural fistula. The cysts occupied 80% to 90% of the crainal cavity. There was severe atrophy and malformation of the underlying brain, suggesting that its development had been disturbed at an early stage of gestation. The clinical and radiologic findings were indistinguishable from those of hydranencephaly.

摘要

两名婴儿患有双侧先天性硬膜下囊肿，伴有脑破坏性孔洞脑畸形和脑脊液-硬膜下瘘。囊肿占据颅腔的80%至90%。其下方的大脑存在严重萎缩和畸形，提示其发育在妊娠早期就受到了干扰。临床和放射学表现与积水性无脑畸形难以区分。