Lucaya J, Enriquez G, Delgado R, Castellote A
AJR Am J Roentgenol. 1984 Mar;142(3):471-4. doi: 10.2214/ajr.142.3.471.
Of 11,500 children who underwent excretory urography during a 17-year period, three were found to have the rare renal malformation infundibulopelvic stenosis, characterized by caliceal dilatation, infundibular stenosis, and hypoplasia or stenosis of the renal pelvis. The contralateral kidney was absent in two cases and normal in the other. Voiding cystourethrograms were normal in all three. Renal sonography showed a variable degree of caliceal dilatation without associated pelvic dilatation. The diagnosis was confirmed by retrograde ureteropyelography in one case. Two patients were followed for 12 and 18 months, respectively; both remained asymptomatic with normal renal function, and sequential sonographic examinations of their kidneys have shown no significant changes. The third patient died of an unrelated condition. Infundibulopelvic stenosis has highly characteristic radiographic features, and prognosis is good for most affected patients.
在17年期间接受排泄性尿路造影的11500名儿童中，有3名被发现患有罕见的肾畸形——肾盂漏斗部狭窄，其特征为肾盏扩张、漏斗部狭窄以及肾盂发育不全或狭窄。其中2例对侧肾缺如，另1例对侧肾正常。3例患者的排尿性膀胱尿道造影均正常。肾脏超声检查显示不同程度的肾盏扩张，但无肾盂扩张。1例患者经逆行输尿管肾盂造影确诊。2例患者分别随访了12个月和18个月；二者均无症状，肾功能正常，肾脏的系列超声检查未显示明显变化。第3例患者死于无关疾病。肾盂漏斗部狭窄具有高度特征性的影像学表现，大多数受累患者的预后良好。
