D'Alessandro R, Tinuper P, Lozito A, Sacquegna T, Cortelli P, Pazzaglia P
Ital J Neurol Sci. 1983 Sep;4(3):335-7. doi: 10.1007/BF02043488.
In a case characterized by progressive generalized dystonic paraplegia with amyotrophy and mental deficiency, CT scanning shows a bilateral lenticular nucleus hypodensity. A similar picture can be found in Wilson disease. However, this patient presented no biochemical, hepatic or ocular abnormalities.