Hyams J S, Conard F U, Hight D W
J Pediatr Gastroenterol Nutr. 1983 Nov;2(4):701-4. doi: 10.1097/00005176-198311000-00022.
Life-threatening ascites developed in a 4-month-old infant with biliary atresia 1 month after hepatic portoenterostomy. Although initially ascribed to progressive liver failure, the ascites was subsequently found to be partially caused by portal vein thrombosis. Documented recanalization of the portal venous system was accompanied by resolution of the ascites. Refractory ascites in patients with biliary atresia generally signals end-stage cirrhosis and consideration of liver transplantation. Portal vein patency should be evaluated before referral of such patients for this procedure.
一名4个月大的胆道闭锁婴儿在肝门肠吻合术后1个月出现危及生命的腹水。尽管最初认为腹水是由进行性肝衰竭引起的，但随后发现部分原因是门静脉血栓形成。门静脉系统记录到的再通伴随着腹水的消退。胆道闭锁患者的难治性腹水通常预示着终末期肝硬化，并需要考虑肝移植。在将此类患者转诊进行该手术之前，应评估门静脉通畅情况。
