Hurtado del Rio D, Holden Barker A M
Arch Inst Cardiol Mex. 1978 Mar-Apr;48(2):362-72.
The author's experience in the association of right aortic arch and congenital cardiac malformations is reported. We found 56 cases out of 1200 congenital cardiac malformations which constitutes 4.6%. In the classification of Knight and Edwards, type I right aortic arch was the most frequent (96%) and it was associated principally with Tetralogy of Fallot (46%), transposition of the great vessels (14.3%), truncus arteriosus (12%), tricuspid atresia (10.7%) and complex cardiac malformations associated with the syndrome of visceral heterotaxy (10.7%). In type II and type III we found only one case of each and these were associated with pulmonary valvular stenosis, atrial septal defect and ventricular septal defect. It is noted that the right aortic arch has never been associated with total anomalous pulmonary venous return nor with mitral or aortic valvular malformations.
本文报告了作者在右位主动脉弓与先天性心脏畸形关联方面的经验。我们在1200例先天性心脏畸形中发现了56例右位主动脉弓，占4.6%。在奈特（Knight）和爱德华兹（Edwards）的分类中，I型右位主动脉弓最为常见（96%），主要与法洛四联症（46%）、大动脉转位（14.3%）、永存动脉干（12%）、三尖瓣闭锁（10.7%）以及与内脏异位综合征相关的复杂心脏畸形（10.7%）有关。在II型和III型中，我们各发现1例，分别与肺动脉瓣狭窄、房间隔缺损和室间隔缺损有关。值得注意的是，右位主动脉弓从未与完全性肺静脉异位引流相关，也未与二尖瓣或主动脉瓣畸形相关。
