De Vere-Tyndall A, Macauley D, Ansell B M
Clin Rheumatol. 1983 Dec;2(4):415-8. doi: 10.1007/BF02041564.
Two children suffering from systemic juvenile chronic arthritis (JCA) complicated by acute disseminated intravascular coagulation (DIC) are described. One had a fatal outcome with acute renal failure and cerebral haemorrhage; the other recovered. Early recognition and treatment of the underlying cause - usually an infection - as well as replacement of clotting factors are important in management.
本文描述了两名患有全身性幼年慢性关节炎(JCA)并并发急性弥散性血管内凝血(DIC)的儿童。其中一名儿童因急性肾衰竭和脑出血而死亡;另一名儿童康复。早期识别和治疗潜在病因——通常是感染——以及补充凝血因子在治疗中很重要。