Mafee M F, Selis J E, Yannias D A, Valvassori G E, Pruzansky S, Applebaum E L, Capek V
Radiology. 1984 Feb;150(2):427-34. doi: 10.1148/radiology.150.2.6691097.
The ears of 47 selected patients with congenital sensorineural hearing loss were examined with complex-motion tomography. The patients were divided into 3 general categories: those with a recognized syndrome, those with sensorineural hearing loss unrelated to any known syndrome, and those with microtia. A great variety of inner ear anomalies was detected, but rarely were these characteristic of a particular clinical entity. The most common finding was the Mondini malformation or one of its variants. Isolated dysplasia of the internal auditory canal or the vestibular aqueduct may be responsible for sensorineural hearing loss in some patients. Patients with microtia may also have severe inner ear abnormalities despite the fact that the outer and inner ears develop embryologically from completely separate systems.
对47例先天性感音神经性听力损失患者的耳部进行了复杂运动断层扫描检查。这些患者分为三大类：患有已确认综合征的患者、患有与任何已知综合征无关的感音神经性听力损失的患者以及患有小耳畸形的患者。检测到了各种各样的内耳异常，但这些异常很少是特定临床实体的特征。最常见的发现是Mondini畸形或其变体之一。内耳道或前庭导水管的孤立发育异常可能是某些患者感音神经性听力损失的原因。尽管外耳和内耳在胚胎学上由完全独立的系统发育而来，但患有小耳畸形的患者也可能有严重的内耳异常。
